스테로이드에 반응하지 않은 비강에 발생한 면역글로불린 G4 연관 경화성 질환 1례
- Title
- 스테로이드에 반응하지 않은 비강에 발생한 면역글로불린 G4 연관 경화성 질환 1례
- Other Titles
- A Case of Immunoglobulin G4-Related Sclerosing Disease not Responded to Steroid in Nasal Cavity
- Author
- 정진혁
- Keywords
- IgG4 연관 경화성 질환; 형질세포; 비강; 부비동; IgG4-related sclerosing disease; Plasma cell; Nasal cavity; Paranasal sinus
- Issue Date
- 2017-12
- Publisher
- 대한비과학회
- Citation
- Journal of Rhinology, v. 24, no. 2, page. 138-142
- Abstract
- IgG4-related sclerosing disease was first discovered when researching autoimmune pancreatitis. It is an autoimmune disease that causes fibrosis on the pancreas, bile duct, gall bladder, salivary glands, and lungs. It is rarely reported in the nasal cavity.The diagnosis of IgG4-related sclerosing disease is based on biopsy findings demonstrating the characteristic histopathologic findings and immunohistochemical staining. IgG4-related sclerosing disease shows good response to high-dose steroid therapy.However, some patients do not respond to this treatment. Azathioprine or rituximab can be helpful in such case. We report our experience with IgG4-related sclerosing disease treated with azathioprine for 2 years, along with a related literature review.
- URI
- https://synapse.koreamed.org/DOIx.php?id=10.18787/jr.2017.24.2.138https://repository.hanyang.ac.kr/handle/20.500.11754/116665
- ISSN
- 1229-1498; 2384-4361
- DOI
- 10.18787/jr.2017.24.2.138
- Appears in Collections:
- COLLEGE OF MEDICINE[S](의과대학) > MEDICINE(의학과) > Articles
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